AJP - Lung Cellular and Molecular Physiology -- Said 291 (4): L547 Table 1

Table 1. Diagnostic classification of pulmonary hypertension

Pulmonary arterial hypertension Familial PAH, idiopathic (Primary) PAH

PAH associated with collagen vascular disease, sarcoidosis, congenital left-to-right shunt, portal hypertension, human immunodeficiency infection, appetite-suppressant drugs, pulmonary veno-occlusive disease, pulmonary capillary hemangiomatosis, and persistent pulmonary hypertension of the newborn

PH with left heart disease Left-sided atrial, ventricular, or valvular heart disease

PH associated with chronic lung disease or hypoxemia Chronic obstructive pulmonary disease, interstitial lung disease, sleep-disordered breathing, alveolar hypoventilation syndromes, prolonged residence at high altitude

PH due to chronic thrombo-embolic disease

PH, pulmonary hypertension; PAH, pulmonary arterial hypertension. [Adapted from Humbert (50).]



Pulmonary arterial hypertension	Familial PAH, idiopathic (Primary) PAH
	PAH associated with collagen vascular disease, sarcoidosis, congenital left-to-right shunt, portal hypertension, human immunodeficiency infection, appetite-suppressant drugs, pulmonary veno-occlusive disease, pulmonary capillary hemangiomatosis, and persistent pulmonary hypertension of the newborn
PH with left heart disease	Left-sided atrial, ventricular, or valvular heart disease
PH associated with chronic lung disease or hypoxemia	Chronic obstructive pulmonary disease, interstitial lung disease, sleep-disordered breathing, alveolar hypoventilation syndromes, prolonged residence at high altitude
PH due to chronic thrombo-embolic disease